Perivascular Epithelioid Cell Tumor of Gastrointestinal Tract
نویسندگان
چکیده
treatment strategies, an not yet been confirm PEComas arising in t Editor: Chun-xia Cao. Received: August 3, 2014; revised and accepted: December 3, 2014. From the Guangdong Institute of Gastroenterology and the Sixth Affiliated Hospital, (BL, CW, JZ, MS, XZ, SS, JW, HL); Guangdong Key Laboratory of Colorectal and Pelvic Floor Diseases, (BL, CW, JZ, MS, XZ, JW, HL); Institute of Human Virology, (BL, CW, JZ, MS, XZ, HL) Key Laboratory of Tropical Disease Control (Ministry of Education); Sun Yat-sen University, Guangzhou (BL, CW, JZ, MS, XZ, HL); Dongguan Health School, Dongguan, China (BL); Department of Human Genetics, Radboud University Medical Center, Nijmegen, The Netherlands (JZ, RPK, AGK); and Advanced Clinical Research Center, Institute of Medical Science, University of Tokyo, Tokyo, Japan (AI). Correspondence: Huanliang Liu, Guangdong Institute of Gastroenterology, Sun Yat-sen University, 26 Yuan Cun Er Heng Road, Guangzhou, Guangdong 510655, China (e-mail: [email protected]); Jianping Wang, The Sixth Affiliated Hospital, Sun Yat-sen University, 26 Yuan Cun Er Heng Road, Guangzhou, Guangdong 510655, China (email: [email protected]). Grant Support: This study was supported by Science and Information Technology Bureau of Guangzhou, Guangdong (2011J5200009); Guangdong Provincial Department of Science and Technology (2012B050500004); Guangdong Innovative Research Team Program (2009010058); Overseas Excellent Professor Project, Ministry of Education; ‘‘985 Project’’ of Sun Yat-sen University, Guangdong Translational Medicine Public Platform (4202037); National Key Clinical Discipline; and Japan Ministry of Education, Culture, Sports, Science and Technology (MEXT) for Program of Japan Initiative for Global Research Network on Infectious Diseases (J-GRID). The authors do not have any possible conflicts of interest. Copyright # 2015 Wolters Kluwer Health, Inc. All rights reserved. This is an open access article distributed under the Creative Commons Attribution License 4.0, which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited. ISSN: 0025-7974 DOI: 10.1097/MD.0000000000000393
منابع مشابه
Perivascular epithelioid cell tumor of the rectum: report of a case and review of the literature
We report a case of perivascular epithelioid cell tumor arising in the rectum of a 55-year-old woman. The tumor was treated by transanal endoscopic microsurgery. After 1 year follow-up, the patient is alive with no radiologic or endoscopic evidence of recurrence. Perivascular epithelioid cell tumor is a rare mesenchymal tumor characterized by co-expression of melanocytic and smooth muscle marke...
متن کاملMalignant Perivascular Epithelioid Cell Tumor of the Esophagus
Malignant perivascular epithelioid cell tumor (PEComa) is a rare tumor composed of hybrid tumor cells characterized by immunoreactivity for both melanocytic and smooth muscle markers. This paper describes the uncommon esophageal location of an 8 cm PEComa in a 75-year-old Caucasian man who was presented with ingravescent dysphagia. Although PEComas arising within the gastrointestinal tract are ...
متن کاملA systematic review: perivascular epithelioid cell tumor of gastrointestinal tract
Perivascular epithelioid cell tumor (PEComa) is a rare entity with distinctive morphology and of expressing myomelanocytic markers. Gastrointestinal tract (GI) is one of the most common anatomic sites of origin and counts for 20% to 25% of all reported cases of perivascular epithelioid cell tumors not otherwise specified (PEComas-NOS). However, the biologic behavior of perivascular epithelioid ...
متن کاملPerivascular epithelioid cell tumor of the ileum. A case report.
Perivascular epithelioid cell tumors (PEComa) are tumors of perivascular epithelioid cells with immunohistochemical features of smooth muscle and melanocytic tumors. The PEComa of the gastrointestinal tract is rare. The treatment is surgical, although there are data that suggest a good response to rapamycin.
متن کاملPerivascular epithelioid cell tumor of the descending colon mimicking a gastrointestinal stromal tumor: a case report
BACKGROUND We present a case of perivascular epithelioid cell tumor (PEComa), which clinically and histologically mimics a gastrointestinal stromal tumor (GIST). CASE PRESENTATION A 42-year-old woman was found to have a mass in the left flank during her annual medical checkup. Computed tomography examination revealed a submucosal tumor of the descending colon. Surgeons and radiologists suspec...
متن کاملPerivascular epithelioid cell tumor in the duodenum: challenge in differential diagnosis.
Defined as a family of scarce mesenchymal neoplasm which distinctively co-express melanocytic markers and muscle markers, perivascular epithelioid cell tumors (PEComas) have been reported almost everybody site. Perivascular epithelioid cell tumors-not otherwise specified (PEComas-NOS) arising in the gastrointestinal (GI) tract are still restricted into sporadic case reports. Herein we present a...
متن کامل